Values CatLog read from this paper
Km defect in neuraminidase of dysmorphic type sialidosis with and without beta-galactosidase deficiency
PMID 6811161doi:10.1016/0009-8981(82)90167-xOpen in Browse
The paper itself is not on this site: read it at the publisher. This page lists only the values CatLog read from it.
CatLog read 32 records (32 values) from this paper: neuraminidase (lysosomal sialidase), beta-galactosidase from Homo sapiens.
Read from the paper by an AI model and checked against the paper by a second, separate AI run; code converted the units. Values are in CatLog's units; each record opens in Browse with the line the paper prints and the checks.
| Enzyme | Organism | Substrate | kcat (s⁻¹) | Km (mM) | kcat/Km (mM⁻¹ s⁻¹) | Conditions | Open record |
|---|---|---|---|---|---|---|---|
| beta-galactosidase | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.253 | — | Open record: beta-galactosidase, 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line A.R. (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.225 | — | Open record: beta-galactosidase variant patient cell line A.R. (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line E.H. (mucolipidosis II; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.268 | — | Open record: beta-galactosidase variant patient cell line E.H. (mucolipidosis II; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line F.A. (mucolipidosis II; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.269 | — | Open record: beta-galactosidase variant patient cell line F.A. (mucolipidosis II; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 1494 (mucolipidosis III; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.23 | — | Open record: beta-galactosidase variant patient cell line GM 1494 (mucolipidosis III; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 1718 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.232 | — | Open record: beta-galactosidase variant patient cell line GM 1718 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 2048 (mucolipidosis IV; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.229 | — | Open record: beta-galactosidase variant patient cell line GM 2048 (mucolipidosis IV; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 2527 (mucolipidosis IV; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.255 | — | Open record: beta-galactosidase variant patient cell line GM 2527 (mucolipidosis IV; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 2629 (mucolipidosis IV; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.247 | — | Open record: beta-galactosidase variant patient cell line GM 2629 (mucolipidosis IV; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line GM 2685 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.278 | — | Open record: beta-galactosidase variant patient cell line GM 2685 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line M.L. (sialidosis 1 (normomorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.247 | — | Open record: beta-galactosidase variant patient cell line M.L. (sialidosis 1 (normomorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line N.G. (mucolipidosis II; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.225 | — | Open record: beta-galactosidase variant patient cell line N.G. (mucolipidosis II; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line T.R. (GM1 gangliosidosis II; mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.245 | — | Open record: beta-galactosidase variant patient cell line T.R. (GM1 gangliosidosis II; mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line [15] (sialidosis 1 (normomorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.301 | — | Open record: beta-galactosidase variant patient cell line [15] (sialidosis 1 (normomorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| beta-galactosidasevariant patient cell line [16] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized) | Homo sapiens | 4-methylumbelliferyl beta-D-galactopyranoside | — | 0.296 | — | Open record: beta-galactosidase variant patient cell line [16] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized), 4-methylumbelliferyl beta-D-galactopyranoside | |
| neuraminidase (lysosomal sialidase) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.136 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line A.R. (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 1.19 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line A.R. (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line B.J. (sialidosis 1 (normomorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.144 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line B.J. (sialidosis 1 (normomorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line F.A. (mucolipidosis II; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.151 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line F.A. (mucolipidosis II; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 1494 (mucolipidosis III; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.123 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 1494 (mucolipidosis III; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 1718 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 1.48 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 1718 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 2048 (mucolipidosis IV; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.152 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 2048 (mucolipidosis IV; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 2065 (mucolipidosis III; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.149 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 2065 (mucolipidosis III; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 2527 (mucolipidosis IV; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.151 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 2527 (mucolipidosis IV; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line GM 2685 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 1.12 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line GM 2685 (sialidosis 2 infantile onset (dysmorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line M.K. (GM1 gangliosidosis I; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.143 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line M.K. (GM1 gangliosidosis I; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line M.L. (sialidosis 1 (normomorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.148 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line M.L. (sialidosis 1 (normomorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line N.G. (mucolipidosis II; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.129 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line N.G. (mucolipidosis II; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line T.R. (GM1 gangliosidosis II; mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.137 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line T.R. (GM1 gangliosidosis II; mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line [15] (sialidosis 1 (normomorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 0.154 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line [15] (sialidosis 1 (normomorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line [16] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 1.01 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line [16] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |
| neuraminidase (lysosomal sialidase)variant patient cell line [17] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized) | Homo sapiens | 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid | — | 1.05 | — | pH 4.3, 37 °C | Open record: neuraminidase (lysosomal sialidase) variant patient cell line [17] (sialidosis 2 juvenile onset (dysmorphic); mutation not characterized), 2-(4-methylumbelliferyl)-alpha-D-N-acetylneuraminic acid |